Periodontitis May Deteriorate Sinus of Valsalva Dilatation in Marfan Syndrome Patients

Marfan syndrome with a giant noncoronary sinus of Valsalva aneurysm

Once presented in 2011 by Dayi SU et al. our case is a 30-year-old woman with Marfan syndrome who had undergone aortic valve replacement due to severe aortic regurgitation secondary to dilatation of the aortic root in 2000 and supracoronary aortic replacement due to Stanford type A dissection in 2002 with subsequent dilatation of sinus of Valsalva. When described by Dayi SU et al. the size of t...

Sinus of valsalva aneurysm in Blau's syndrome

Blau syndrome is a rare granulomatous disorder inherited in an autosomal dominant manner characterized by the early appearance of granulomatous arthritis, skin rash and anterior uveitis. There are very few data on the cardiovascular manifestations of Blau syndrome. Here we report the first case of sinus of valsava aneurysm in Blau syndrome. In isolated unruptured aneurysms of a sinus of Valsalv...

Pregnancy-associated aortic dilatation or dissection in Japanese women with Marfan syndrome.

BACKGROUND Aortic dilatation and dissection are severe complications of pregnancy that may cause maternal death. The purpose of the present study was to investigate risk factors for aortic dilatation or dissection in pregnant Japanese women with Marfan syndrome. METHODS AND RESULTS A total of 28 patients with Marfan syndrome were investigated retrospectively during pregnancy and after deliver...

Treacher Collins syndrome: sinus of Valsalva aneurysm.

Abdominal aortic dilatation during pregnancy in Marfan syndrome.

We present the case of a 29-year-old pregnant woman with Marfan syndrome who presented an aortic root diameter of <45 mm at the start of gestation with no other abnormalities. She had been diagnosed of Marfan syndrome 2 years previously as a result of a family study. The patient underwent a follow-up cardiologic examination before becoming pregnant. At that time, the aortic root diameter at the...